Idiopathic Pulmonary Fibrosis

Idiopathic Pulmonary Fibrosis is a type of idiopathic interstitial pneumonia of unknown origin that causes lung fibrosis and restrictive lung disease. It characteristically involves only the lung and has no extrapulmonary manifestations except clubbing.

Dry cough, Exertional dyspnea, Malaise, Weight loss, Arthralgia, Finger clubbing, Cyanosis

Idiopathic (unknown cause)

Older age group, Male gender, Genetics, Smoking, Occupational dust or fume exposure

Full blood count, Arterial blood gases, C-reactive protein, Immunoglobulins, ANA rheumatoid factor, Chest X-ray, CT chest, Spirometry, Bronchoalveolar lavage, Lung biopsy

Oxygen therapy, Pulmonary rehabilitation, Steroid therapy, Lung transplantation